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Rheumatology

Behçet's Disease

Recurrent oral + genital ulcers + uveitis + skin lesions — variable systemic involvement (vascular, neuro, GI), corticosteroid + steroid-sparing.

Source: EULAR 2018; ISG 1990 criteria

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info

ISG Criteria

Recurrent oral ulceration (≥3/year) + 2 of: • Recurrent genital ulceration. • Eye disease (anterior / posterior uveitis, retinal vasculitis). • Skin lesions (erythema nodosum, pseudofolliculitis, papulopustular). • Positive pathergy test (sterile pustule at site of needle prick within 24–48h). Common along Silk Road (Turkey, Mediterranean, Middle East, Far East). HLA-B51 association.

Related

Curated clinical cross-links plus same-class fallbacks.

Decision support only. Always apply local guidelines and clinical judgement.