PaediatricsHaematology
Paediatric Sickle Cell Crisis
RCPCH/BSH — recognition of vaso-occlusive crisis, fever in sickle (sepsis risk), acute chest syndrome, splenic sequestration, stroke.
Source: BSH 2018; RCPCH
Step 1 of ~7
info
Initial Approach
All children with known sickle cell disease (HbSS, HbSC, HbSβ) presenting acutely require immediate assessment + early haematology contact. ABCDE; SpO₂; urine output; weight; pain assessment; FBC + reticulocytes + group & save; blood culture if any fever; Hb critical (compare to baseline). Verify all paediatric drug doses against BNFc.
Related
Curated clinical cross-links plus same-class fallbacks.
Drugs
- Hydroxycarbamide (Hydroxyurea) · Cytoreductive agent / Sickle cell disease / CML
- Crizanlizumab · P-selectin Inhibitor — Sickle Cell Disease
- Voxelotor · Haemoglobin S Polymerisation Inhibitor — Sickle Cell Disease
- Paracetamol (Paediatric) · Analgesic / Antipyretic — First-Line Pain and Fever in Children
- Prednisolone (Paediatric) · Corticosteroid — Asthma Exacerbation / Croup / Nephrotic Syndrome / IBD
- Ceftriaxone (Paediatric) · Third-Generation Cephalosporin — Meningitis / Sepsis / Community-Acquired Pneumonia
Decision support only. Always apply local guidelines and clinical judgement.