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Cardiology

Adult Congenital Heart Disease — ED Presentation

Approach to an ACHD patient in ED — critical considerations for Eisenmenger, Fontan, single-ventricle, transposition variants.

Source: ESC 2020 ACHD; ACC/AHA 2018 ACHD

Step 1 of ~7
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Initial Approach — Engage ACHD Centre Early

Always involve regional ACHD centre early — physiology often counter-intuitive. Establish: prior repair (palliative, complete, or staged), residual lesions, cyanosis, baseline saturations, arrhythmia history, current medications. Echo expert review essential. Bloods: FBC (chronic erythrocytosis if cyanotic — avoid routine venesection), U&E, BNP, troponin, INR if anticoagulated.

Related

Curated clinical cross-links plus same-class fallbacks.

Decision support only. Always apply local guidelines and clinical judgement.